Title

A unique case of unilateral synophthalmia

Authors

A. D. Proia

Document Type

Article

Date of Publication

11-1-2012

Publication Title

Pediatric and Developmental Pathology

First Page

130

Last Page

133

Abstract

Developmental anomalies resulting in a single eye (cyclopia) or fusion of the eyes (synophthalmia) are rare. Examples of unilateral synophthalmia—in which there are 1 normal and 2 fused eyes from 3 anlagen in 2 orbits, 1 lateral proboscis, and 3 optic nerves—are even more rare. Herein, I report a unique fetus with unilateral synophthalmia that was not associated with a lateral proboscis but instead had an extra cerebral hemisphere. I postulate that the unilateral synophthalmia, accessory cerebral hemisphere, and minor structural abnormalities in the skull base were the result of failure in separating a monozygous twin, a situation similar to that postulated as the cause of fetus in fetu.

DOI

https://doi.org/10.2350/10-03-0809-CR.1

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