Distinct, bilateral epithelioid hemangioma of the orbit

Introduction : Epithelioid hemangioma (EH) is a benign abnormal proliferation of endothelial cells usually arising in the head and neck region and presenting clinically as raised cutaneous lesions. EH rarely involves the orbit and has not been reported to occur bilaterally. Case : A healthy 38 year old female developed sequential proptosis of each orbit over the course of several months. The patient underwent excisional biopsy confirming the diagnosis of EH in each orbit. She was treated with a course of high dose steroids and has been stable at 13 months following the most recent excision. Conclusion : This is the first reported case of bilateral EH.