Atypical lymphocytic angiitis of the optic nerve and central nervous system

Primary angiitis of the central nervous system (PACNS), also known as primary vasculitis of the central nervous system , is a rare, poorly understood, and often fatal disorder. ^{1 , 2} Although the association of PACNS with optic neuropathy has been documented, ^{3 - 5} this is the first report to our knowledge of visual loss with histopathologic involvement of the optic nerves.